Adult onset dermatomyositis associated with lipodystrophy and underlying calcinosis: Case report
نویسندگان
چکیده
Dermatomyositis is an idiopathic inflammatory myopathy, with skin manifestations. A less frequently recognized but clinically important complication of dermatomyositis is lipodystrophy (LD), and associated metabolic abnormalities that increasingly recognized as complications of juvenile dermatomyositis. Lipodystrophy is less frequently reported in adult onset dermatomyositis.In this paper we are presenting a case of adult onset dermatomyositis associated with lipodystrophy and underlying localized calcinosis; at the exact distribution of lipodystrophy.
منابع مشابه
Calcific panniculitis and nasopharyngeal cancer-associated adult-onset dermatomyositis: a case report and literature review
Panniculitis is an uncommon cutaneous manifestation in dermatomyositis. It not only occurs in idiopathic dermatomyositis, but also rarely occurs in the setting of malignancy-associated dermatomyositis. Calcinosis cutis is also less likely to be found in adult-onset dermatomyositis. In malignancy-associated dermatomyositis, panniculitis can precede, concur, or follow the diagnosis of malignancy....
متن کاملCalcinosis as a complication of juvenile dermatomyositis (JDM)
Results 17/42 developed calcinosis associated with earlier onset of the disease, male predominance and chronic. Calcium deposits were classified as: superficial nodular, deep nodular, mass, linear or mixed deposits and calcinosis universalis. 80% had two or more types of deposits. The anatomical areas more frequently affected were the thighs and forearms. Complications included: drainage, chron...
متن کاملCalcinosis and lipodystrophy: clinical presentation of 10 years non-treated juvenile dermatomyositis – case report
Methods We describe a 13,5 y old girl presented (april 2011) with extensive calcinosis and lipodystrophy, which were lasting for 10 years, without any treatment. General, musculoskeletal, pulmological and orthodontist evaluations were undertaken. Investigations included multiple radiographs of the calcified regions and chest X-ray, computed-tomography of the lungs, MRI of pelvis, coxofemoral an...
متن کاملTherapy of calcinosis universalis complicating adult dermatomyositis.
Although frequent in juvenile dermatomyositis, calcinosis is a rare finding in adult dermatomyositis. It has been associated with disease activity and delayed treatment. It is more common in later phases of the disease, in sites under chronic stress and trauma. Calcinosis has been associated with inflammation but information about its pathogeny continues to evolve as we learn more about the und...
متن کاملPredictors of acquired lipodystrophy in juvenile-onset dermatomyositis and a gradient of severity.
We describe the clinical features of 28 patients with juvenile dermatomyositis (JDM) and 1 patient with adult-onset dermatomyositis (DM), all of whom developed lipodystrophy (LD) that could be categorized into 1 of 3 phenotypes, generalized, partial, or focal, based on the pattern of fat loss distribution. LD onset was often delayed, beginning a median of 4.6 years after diagnosis of DM. Calcin...
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